Year: 2023 | Month: September | Volume: 10 | Issue: 9 | Pages: 84-88
DOI: https://doi.org/10.52403/ijrr.20230910
Congenital Cystic Adenomatoid Malformation of Lung - Case Series
Dr. Jonnadula Pratima1, Dr. K. Durga2, Dr. G. Bhavana3, Dr. G. Sai Subrahmanyam4, Dr. G. Divya Tejaswi5
1Department of Pathology, 2Department of Paediatric Surgery,
Narayana Medical College, Dr. Y.S.R. University of Health Sciences, Nellore, India
Corresponding Author: Dr. Jonnadula Pratima
ABSTRACT
Congenital cystic adenomatoid malformation (CCAM) is a rare entity with unexplained cause that effects the distal bronchi. It accounts for 25% of congenital pulmonary malformations with surgical excision as the treatment of choice. The mortality rate of patients with CCAM ranges from 9 to 49% if diagnosed prenatally. The outcome of a patient mainly depends on the presence of hydrops foetalis, microscopic type of CCAM, and the size of the lesions. The mainstay treatment of CCAM is surgical excision of the lesion which prevents complications of repeated infections, pneumothorax, and malignancy. We present 2 cases one is 5-month-old male child and other 8-month female child admitted to hospital with shortness of breath and poor suckling who was evaluated for respiratory distress. Clinically diagnosed as pneumonia, CT chest showed a cystic malformation in right lower lobe of lung and excision was done. Specimens were sent for histopathological examination and was diagnosed as congenital cystic adenomatoid malformation.
Keywords: congenital cystic adenomatoid malformation, infant, lobectomy
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